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- Title
Post Partum Acute Intermittent Porphyria: A Case Report.
- Authors
Gaurav, Tomar; Sethi, Ashish; Kriplani, T. C.; Narang, Neeraj
- Abstract
Porphyrias are inherited disorders, each involving a specific enzyme in heme biosynthetic pathways. These are classified as hepatic or erythropoietic depending on the primary site of overproduction and accumulation of porphyrin. Hepatic porphyria manifested with neurological sign & symptoms while manifested with neurological sign & symptoms while erythro erythropoietic porphyrias cause cutaneous photosensitivity. Acute intermittent porphyria, one of the hepatic porphyria is the most severe form of the disease, with gastrointestinal and neuropsychiatric manifestations, such as neuropathic abdominal pain, nausea, vomiting, peripheral neuropathy (motor, sensory, and autonomic), hypertension, seizures, mental disturbances. Here is a rare case of acute intermittent porphyria in which the patient had a in which the patient had a generalized seizure and progressive paralysis in the puerperium. Proper management will dramatically improve the outcome in this otherwise debilitating and potentially life-threatening disease.
- Publication
Indian Anaesthetists' Forum, 2010, p1
- ISSN
2589-7934
- Publication type
Academic Journal